Vasculitides

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Large-vessel vasculitis

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See Giant cell arteritis

Takayasu arteritis

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Medium-vessel vasculitis

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See Polyarteritis nodosa
Also add Thromboangiitis obliterans

Clinical features


  • Migratory superficial thrombophlebitis (recurrent): often seen prior to the onset of limb ischemia
    • Tender nodules along the course of the affected vein
  • Raynaud phenomenon
  • Chronic or acute limb ischemia: may progress from distal to proximal vessels
    • Intermittent claudication
    • Pain at rest, cool extremities, and/or diminished or absent pulses
    • Ulceration and/or gangrene of fingertips and/or toes (digits may autoamputate)

Small-vessel vasculitis

ANCA-associated small-vessel vasculitis

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See Granulomatosis with polyangiitis

Granulomatosis with polyangiitis (Wegener granulomatosis)

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Microscopic polyangiitis

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Non-ANCA-associated small-vessel vasculitis

IgA vasculitis, also known as Henoch-Schönlein purpura