Epidemiology

Most common cause of nephrotic syndrome in adults, especially in African American and Hispanic populations


Etiology

  • HIV (HIV-associated nephropathy)
  • Heroin use
  • Sickle cell disease
  • Massive obesity
  • Pamidronate, interferon treatment

Pathophysiology

Injury to podocytes leads to effacement of foot processes and subsequent sclerosis and hyalinosis.


Clinical features


Diagnostics

  • LM: segmental sclerosis and hyalinosis
  • EM: effacement of podocyte foot processes (similar to minimal change disease)

Treatment

  • Initial management: supportive therapy including an RAAS inhibitor (i.e., ACEI or ARB).
  • Consider immunosuppressive therapy for all patients with nephrotic syndrome due to FSGS.
    • Prednisone