Etiology


Pathophysiology

  • A specific form of Polymorphic Ventricular Tachycardia occurring in the context of a prolonged QT interval.
  • Characterized by QRS complexes that “twist” around the isoelectric line (Torsades de pointes = twisting of the points).
  • Mechanism: Prolonged repolarization leads to Early Afterdepolarizations (EADs), triggering re-entrant circuits.
  • Can progress to Ventricular Fibrillation (VF) and sudden cardiac death (SCD).

Clinical features

  • Often asymptomatic
  • Cardiovascular features
    • Palpitations
    • Tachycardia (HR ≥100/min; typically regular)
    • Chest pain/pressure
    • Dyspnea, orthopnea
    • Symptoms of reduced cardiac output
      • Dizziness
      • Hypotension
      • Syncope
      • Cardiogenic shock and loss of consciousness
  • Cardiac arrest

Diagnostics

  • Polymorphic VT with QRS complexes that typically appear to twist around the isoelectric line, usually in self-limiting bursts
  • Often preceded by bigeminy and followed by several premature ventricular contractions
  • R-on-T phenomenon may also be seen.

Treatment

  1. Hemodynamically Unstable (Shock, unconscious, pulseless):
    • Immediate unsynchronized cardioversion (defibrillation) & CPR per ACLS protocol.
  2. Hemodynamically Stable:
    • First-lineIV Magnesium Sulfate (give even if serum Mg2+ is normal). c
      • Acts as a natural Ca2+ channel blocker. Decreases inward Ca2+ influx Suppresses Early Afterdepolarizations (EADs) Terminates TdP.
  3. Refractory / Recurrent / Bradycardia-induced:
    • Transvenous overdrive pacing OR Isoproterenol infusion (↑ HR shortens the QT interval, terminating the arrhythmia).
  4. Underlying Cause Correction:
    • D/C all QT-prolonging meds immediately.
    • Replete K+ to > 4.0 mEq/L and Mg2+ to > 2.0 mg/dL.
  5. Long-Term (Congenital Long QT):
    • Beta-blockers (propranolol, nadolol) to blunt sympathetic tone.
    • Implantable Cardioverter-Defibrillator (ICD) if recurrent syncope or prior cardiac arrest.