Epidemiology


Etiology


  • Age: Women < 40 yo.
  • Idiopathic: Most common (~90% of cases).
  • Genetic:
    • Turner syndrome (45,X or mosaicism).
    • FMR1 gene premutation (Fragile X syndrome carriers: 55–200 CGG repeats).
  • Autoimmune:
    • Autoimmune polyglandular syndrome (APS type 1 or 2).
    • Concomitant Hashimoto thyroiditis or Addison disease (anti-21-hydroxylase Abs).
  • Iatrogenic/Environmental:
    • Pelvic radiation or chemotherapy (especially alkylating agents like cyclophosphamide).
    • Bilateral oophorectomy or pelvic surgery.
  • Metabolic/Infectious: Galactosemia, viral oophoritis (mumps).

Pathophysiology


Follicular dysfunction or depletion → ↓ estrogen levels → reduced feedback inhibition of estrogen on FSH and LH → ↑ FSH and LH (usually FSH > LH)

Clinical features


  • Amenorrhea or abnormal uterine bleeding
  • Climacteric symptoms such as vaginal dryness, vasomotor symptoms, dyspareunia, and irritability
  • Infertility

Diagnostics


  • Age is < 40 years
  • There has been irregular menstruation for ≥ 3 consecutive months
  • ↑ FSH levels (> 30–40 mIU/mL)
  • ↓ Estradiol levels (< 50 pg/mL)

Differential Diagnostics

  • Functional Hypothalamic Amenorrhea (FHA):
    • Diff: ↓/Normal FSH & LH, low estradiol; associated with low BMI, excessive exercise, eating disorders, or extreme stress.
  • Polycystic Ovary Syndrome (PCOS):
    • Diff: Normal/↑ LH with normal FSH (↑ LH:FSH ratio), hyperandrogenism (hirsutism, acne), polycystic morphology on US, no elevated menopausal FSH.
  • Hyperprolactinemia:
    • Diff: ↑ Prolactin, low/normal gonadotropins, galactorrhea, pituitary adenoma on MRI.
  • Asherman Syndrome (Intrauterine Adhesions):
    • Diff: Normal FSH, LH, and Estradiol; negative withdrawal bleed after estrogen + progesterone challenge; hx of postpartum curettage or endometritis.
  • Physiologic Menopause:
    • Diff: Occurs at normal physiological age (≥ 40 yo, average 51 yo).

Treatment