Clinical features

  • Extraintestinal Manifestations (EIM):
    • Parallel to bowel inflammation (improves with IBD treatment):
      • Peripheral arthritis (type 1: pauciarticular; type 2: polyarticular).
      • Cutaneous: Erythema nodosum (painful, pretibial red nodules).
      • Ocular: Episcleritis.
      • Oral: Aphthous stomatitis.
    • Independent of bowel inflammation (does not correlate with disease activity):
      • Axial arthropathy: Ankylosing spondylitis, sacroiliitis (HLA-B27 associated). c
      • Cutaneous: Pyoderma gangrenosum (deep, necrotic, purulent ulcer with violaceous borders; classic in UC).
      • Ocular: Anterior uveitis (photophobia, eye pain).
      • Hepatobiliary: Primary Sclerosing Cholangitis (PSC) (strongest association with UC; marked by elevated ALP/GGT, bead-like biliary strictures on MRCP).
    • CD-specific metabolic complications:
      • Calcium oxalate nephrolithiasis: Fat malabsorption in terminal ileum -> Ca²⁺ binds unabsorbed fatty acids -> free oxalate absorbed in colon -> hyperoxaluria.
      • Gallstones: Decreased bile salt reabsorption in diseased terminal ileum -> lithogenic bile.
      • Macrocytic anemia: Vitamin B12 deficiency from terminal ileum destruction.