Epidemiology


Etiology


  • The exact cause is unknown, but it’s strongly linked to CNS iron deficiency and subsequent dopamine dysregulation in the basal ganglia.
  • Can be Primary (Idiopathic), often with a positive family history (autosomal dominant), or Secondary.
  • Secondary Causes are high-yield and include:
    • Iron Deficiency Anemia: Most common and well-established secondary cause.
    • Uremia (ESRD): Present in up to 50% of patients on dialysis.
    • Pregnancy: Common, especially in the third trimester, and usually resolves post-delivery.
    • Peripheral neuropathy (e.g., from diabetes).
    • Medications: Antihistaminesantipsychotics (dopamine antagonists), and some antidepressants (SSRIs) can trigger or worsen symptoms.

Pathophysiology


  • The pathophysiology of RLS is incompletely understood but likely involves CNS iron deficiency (even in patients with normal serum iron levels) and abnormalities in dopaminergic transmission.
  • See akathisia, an Extrapyramidal symptoms (EPS)

Clinical features


  • An irresistible urge to move the legs, often accompanied by unpleasant creeping or crawling sensations.
  • Symptoms follow a distinct pattern summarized by the mnemonic “URGE”:
    • Urge to move
    • Rest worsens symptoms
    • Getting up (movement) improves symptoms
    • Evening/night worsening of symptoms (circadian pattern)
  • Leads to significant sleep disturbance and daytime fatigue.
  • Often associated with Periodic Limb Movements of Sleep (PLMS), which are involuntary, brief leg jerks during sleep.

Diagnostics


Treatment


  • Address and treat any underlying secondary cause first (e.g., iron supplementation, optimizing dialysis).
  • First-line pharmacologic agents have shifted according to recent guidelines:
    • Alpha-2-delta calcium channel ligandsGabapentin or pregabalin are now strongly recommended as first-line therapy. They are particularly useful if the patient also has insomnia or neuropathic pain.
  • Dopamine Agonists (pramipexoleropinirole):
    • Previously first-line, but their use is now discouraged for standard, long-term treatment due to the high risk of augmentation. Augmentation is a paradoxical worsening of symptoms with long-term use (earlier onset, increased intensity, spreading to arms).
  • Iron Supplementation:
    • Essential if iron stores are low (Ferritin ≤75 ng/mL).
    • Both oral (ferrous sulfate) and IV iron formulations (ferric carboxymaltose) are used. IV iron may be considered if oral iron is not tolerated or in more severe cases.
  • Refractory Cases:
    • Low-dose opioids may be considered for severe, refractory cases but require cautious use.